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dc.contributor.authorKylat, Ranjit I
dc.contributor.authorWitte, Marlys H
dc.contributor.authorBarber, Brent J
dc.contributor.authorDori, Yoav
dc.contributor.authorGhishan, Fayez K
dc.date.accessioned2019-12-18T18:00:26Z
dc.date.available2019-12-18T18:00:26Z
dc.date.issued2019-11-07
dc.identifier.citationKylat RI, Witte MH, Barber BJ, Dori Y, Ghishan FK. Resolution of Protein-Losing Enteropathy after Congenital Heart Disease Repair by Selective Lymphatic Embolization. Pediatr Gastroenterol Hepatol Nutr. 2019 Nov;22(6):594-600. https://doi.org/10.5223/pghn.2019.22.6.594en_US
dc.identifier.issn2234-8646
dc.identifier.pmid31777727
dc.identifier.doi10.5223/pghn.2019.22.6.594
dc.identifier.urihttp://hdl.handle.net/10150/636445
dc.description.abstractWith improving survival of children with complex congenital heart disease (CCHD), postoperative complications, like protein-losing enteropathy (PLE) are increasingly encountered. A 3-year-old girl with surgically corrected CCHD (ventricular inversion/L-transposition of the great arteries, ventricular septal defect, pulmonary atresia, post-double switch procedure [Rastelli and Glenn]) developed chylothoraces. She was treated with pleurodesis, thoracic duct ligation and subsequently developed chylous ascites and PLE (serum albumin ≤0.9 g/dL) and was malnourished, despite nutritional rehabilitation. Lymphangioscintigraphy/single-photon emission computed tomography showed lymphatic obstruction at the cisterna chyli level. A segmental chyle leak and chylous lymphangiectasia were confirmed by gastrointestinal endoscopy, magnetic resonance (MR) enterography, and MR lymphangiography. Selective glue embolization of leaking intestinal lymphatic trunks led to prompt reversal of PLE. Serum albumin level and weight gain markedly improved and have been maintained for over 3 years. Selective interventional embolization reversed this devastating lymphatic complication of surgically corrected CCHD.en_US
dc.language.isoenen_US
dc.publisherKOREAN SOC PEDIATRIC GASTROENTEROLOGY & NUTRITIONen_US
dc.rightsCopyright © 2019 by The Korean Society of Pediatric Gastroenterology, Hepatology and Nutrition. This is an open-access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (https://creativecommons.org/licenses/by-nc/4.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.en_US
dc.subjectCardiac surgical proceduresen_US
dc.subjectEmbolization, therapeuticen_US
dc.subjectHeart defects, congenitalen_US
dc.subjectLymphatic abnormalitiesen_US
dc.subjectProtein-losing enteropathiesen_US
dc.titleResolution of Protein-Losing Enteropathy after Congenital Heart Disease Repair by Selective Lymphatic Embolizationen_US
dc.typeArticleen_US
dc.contributor.departmentUniv Arizona, Dept Pediat, Coll Meden_US
dc.contributor.departmentUniv Arizona, Coll Med, Dept Surgen_US
dc.identifier.journalPEDIATRIC GASTROENTEROLOGY HEPATOLOGY & NUTRITIONen_US
dc.description.noteOpen access journalen_US
dc.description.collectioninformationThis item from the UA Faculty Publications collection is made available by the University of Arizona with support from the University of Arizona Libraries. If you have questions, please contact us at repository@u.library.arizona.edu.en_US
dc.eprint.versionFinal published versionen_US
dc.source.journaltitlePediatric gastroenterology, hepatology & nutrition
refterms.dateFOA2019-12-18T18:00:26Z


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